Genital ulcer as a new clinical clue to PFAPA syndrome.
Scattoni R, Verrotti A, Rinaldi VE, Paglino A, Carelli A , et al.
Clinical and experimental dermatology •
Vaginal ulcers can be associated with a number of different diseases. We describe two girls who presented genital ulcers as a persistent symptom of PFAPA (periodic fever, aphthous stomatitis, pharyngitis, cervical adenitis) syndrome. The possibility of considering this clinical manifestation as a clue for the diagnosis of PFAPA is discussed.